i 19/59(32%)24/200(12%)0.0006 II 23/59(39%)62/200(32%)0.2511 III 14/59(24%)80/200(40%)0.0224 IV 1/59(2%)(2%)9/200(4.5%)9/200(4.5%)1.000 v 2/59(3%)(3%)(3%)(3%) BULBAR参与18/59(31%)104/200(52%)0.004治疗NO IS IS IS IS IS 23/59(39%)33/200(16.5%)0.0002 CS 26/59(44%)75/200(44%)75/200(37.5%)0.3634 CS+IS 10/59(17%)(17%)(17%)92/200(46%)(46%)(46%)(46%) (20%)100/200(50%)<0.0001中位随访(IQR),第12(5-18)年7(3-12)0.0012