突变VWF突变(36.4%vs 22.6%P = 1,000),FVIII:C/VWF:AG比率(1.24±0.24 vs 1.46±0.27,P = 0.444)和VWFPP/VWFPPP/VWF:AG比率(1.24±0.24 vs 1.36 vs = 1.36 vs 1.36 vs 1.36 vs,爱情和赢得队列。Coorte赢得持续水平的VWF <30 IU/DL的患者经常具有VWF的遗传变异(93.0%),FVIII较高:C/VWF:AG:AG(2.65±1.62)和VWFPP/VWF/VWF:与其他组(6.14±7.05)相比(6.14±7.05)(6.14±7.05)