自发性内部低血压的临床和放射学表现高度可变,许多患者不满足2004年(2018年)国际头痛疾病标准的分类。我们根据病例开发了新的自发颅内低血压诊断标准,我们看到了反映该疾病的可变表现。这些标准在下一个修订分类标准时为变更提供了基础。DIAGNOSTIC CRITERIA CONSIST OF • ORTHOSTATIC HEADACHE • THE PRESENCE OF AT LEAST ONE OF THE FOLLOWING: 1. low opening pressure (≤ 60 mm H2O) 2. sustained improvement of symptoms after epidural blood patching, ***demonstration of an active spinal cerebrospinal fluid leak, 3. cranial magnetic resonance imaging changes of intracranial hypotension (eg, brain sagging or pachymeningeal enhancement);